Fourty-five patients with double-outlet right ventricle(DORV) underwent complete intracardiac repair between July, 1983 and June, 1989.
Patients with complete atrioventricular canal, atrioventricular discordance and univentricular heart were excluded.
The 32 male and 13 female patients ranged in age from months to 15 years (mean 4 years). Thirty-two patients had pulmonary stenosis.
The early mortality was 11.1%(5 /45)
None of 27 died after a completely intraventricular repair.
The mortality was 20%(1 /5) for repair using transanular patch, 20.10(1 /5) for REV operation, 33.3%(1/3) for repair including extracardiac valved conduit, and 509/b(1 /2) for Jatene operation, respectively.
Two modified Fontan procedures were performed without mortality. One died after Senning operation.
Causes of early deaths included high residual right ventricular pressure(one patient) small left atrial and left ventricular volume(one patient), persisting severe pulmonary hypertension (one patient) and low cardiac output of unknown cause (two patients).
Complete heart block developed in one patient.
Two late deaths occurred among the 40 operative survivors (5.0%) from persisting servere pulmonary hypertension and bleeding at reoperation.
Our results indicate that significant defects can be repaired with low mortality and morbidity.
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